Abstract

1. Abstact

Spinal muscular atrophy (SMA) is a neuromuscular disease which has varioous clinical progressions. There are difficulties in the management of anesthesia for this disease. The most common anesthetic risks are airway management and respiratory complications. With this case report, we wanted to review the anesthesia management in patients with this disease. Spinal muscular atrophy (SMA) is a neuromuscular disease manifested by weakness and atrophy of the proximal muscles, which occur due to progressive degeneration of the anterior horn cells of the spinal cord. Genetic transition is observed with autosomal recessive inheritance in 98% of patients and autosomal dominant or X-linked inheritance in 2% [1].