Abstract

1. Abstract

Congenital megacalycosis of Pugivert is a rare clinical entity which denotes presence of dilated calyces most often without any functional abnormality and Segmental mega-ureter implies large, focal segmental ureteral dilatation producing a distorted ureter. Megacalycosis with an ipsilateral segmental mega-ureter is a rarer association of which only a few cases have been reported after its original description. It is diagnosed incidentally or the patient might present with urinary tract infection or calculus formation and usually respond to conservative management.