Abstract

Epithelioid hemangioendothelioma is a rare type of angiogenic tumor composed of Epithelioid endothelial cells, which is characterized by potentially malignancy and metastasis potential. It is mainly seen in adults, while very rare in children. Tumor can be found in soft tissue or other parts,such as liver and lung, however it is rare in the kidneys. The very report is the first case of that tumor is found in the renal pelvis, which contains only 4 cases of EHE in the kidney. This paper reports one case of EHE in the kidney, and reviews the relevant literatures to discuss its clinical characteristics and differential diagnosis points to better understand the disease.