Abstract

Mesenchymal Chondrosarcoma (MC) is a rare and aggressive high-grade malignant tumor of bone and soft tissue which was first described by Lichtenstein and Bernstein in 1959 in a reviewing survey of a 25 unusual benign and malignant chondroid tumors of bone[1]. The incidence is approximately 1% of all chondrosarcoma neoplasms[2]. Extra-skeletal Mesenchymal Chondrosarcoma (EMC) is found in a third of the patient sin a one conducted case series [3]. Primary Renal Extra-skeletal Mesenchymal Chondrosarcoma (PREMC) is extremely rare and to date only twelve cases have been previously reported in the literature (Table 1).