Case of Rare Entity - Parry-Romberg Syndrome

Abstract

Parry-Romberg syndrome (PRS), also known as progressive facial hemyatrophy is a rare clinical entity with prevalence of 1 case on 250  000 of general population [1-3]. It was first described by C.Parry in 1825 and – later – by M.Romberg in 1846 [1,2]. Course of this syndrome ends in atrophy of subcutaneous fat with skin changes, en coupe de sabre sign, in some cases facial muscles wasting, ophthalmic and nervous systems involvement [4-9].